Giant bilateral adrenal myelolipoma with congenital adrenal hyperplasia. (Record no. 5771)
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| 000 -LEADER | |
|---|---|
| fixed length control field | 02292nam a22003017a 4500 |
| 008 - FIXED-LENGTH DATA ELEMENTS--GENERAL INFORMATION | |
| fixed length control field | 201229s20142014 xxu||||| |||| 00| 0 eng d |
| 040 ## - CATALOGING SOURCE | |
| Original cataloging agency | Ovid MEDLINE(R) |
| 099 ## - LOCAL FREE-TEXT CALL NUMBER (OCLC) | |
| PMID | 25140269 |
| 245 ## - TITLE STATEMENT | |
| Title | Giant bilateral adrenal myelolipoma with congenital adrenal hyperplasia. |
| 251 ## - Source | |
| Source | Case Reports in Surgery. 2014:728198, 2014. |
| 252 ## - Abbreviated Source | |
| Abbreviated source | Case Rep Surg. 2014:728198, 2014. |
| 253 ## - Journal Name | |
| Journal name | Case reports in surgery |
| 260 ## - PUBLICATION, DISTRIBUTION, ETC. | |
| Year | 2014 |
| 260 ## - PUBLICATION, DISTRIBUTION, ETC. | |
| Manufacturer | FY2014 |
| 265 ## - SOURCE FOR ACQUISITION/SUBSCRIPTION ADDRESS [OBSOLETE] | |
| Publication status | ppublish |
| 266 ## - Date added to catalog | |
| Date added to catalog | 2020-12-29 |
| 520 ## - SUMMARY, ETC. | |
| Abstract | Myelolipomas are rare and benign neoplasms, predominant of the adrenal glands, consisting of adipose and mature hematopoietic tissue, commonly discovered incidentally with increased use of radiologic imaging. Few cases of giant bilateral adrenal masses are reported, especially in the setting of congenital adrenal hyperplasia (CAH). We report the case of a 39-year-old male with a history of CAH secondary to 21-alpha hydroxylase deficiency on steroids since childhood, self-discontinued during adolescence, presenting with abdominal distension, fatigue, decreased libido, and easy bruising. Imaging revealed giant bilateral adrenal masses. He subsequently underwent bilateral adrenalectomy found to be myelolipomas measuring 30 x 25 x 20 cm on the left and weighing 4.1 kg and 25 x 20 x 13 cm on the right and weighing 2.7 kg. Adrenal myelolipomas are found to coexist with many other conditions such as Cushing's syndrome, Addison's disease, and CAH. We discuss the association with high adrenocorticotropic hormone (ACTH) states and review the studies involving ACTH as proponent leading to myelolipomas. Massive growth of these tumors, as in our case, can produce compression and hemorrhagic symptoms. We believe it is possible that self-discontinuation of steroids, in the setting of CAH, may have resulted in the growth of his adrenal masses. |
| 546 ## - LANGUAGE NOTE | |
| Language note | English |
| 650 ## - SUBJECT ADDED ENTRY--TOPICAL TERM | |
| Topical term or geographic name entry element | IN PROCESS -- NOT YET INDEXED |
| 651 ## - SUBJECT ADDED ENTRY--GEOGRAPHIC NAME | |
| Institution | MedStar Union Memorial Hospital |
| 657 ## - INDEX TERM--FUNCTION | |
| Medline publication type | Journal Article |
| 700 ## - ADDED ENTRY--PERSONAL NAME | |
| Local Authors | Al-Bahri, S |
| 700 ## - ADDED ENTRY--PERSONAL NAME | |
| Local Authors | Lowentritt, B |
| 700 ## - ADDED ENTRY--PERSONAL NAME | |
| Local Authors | Nasrallah, D V |
| 790 ## - Authors | |
| All authors | Al-Bahri S, Lowentritt B, Nasrallah DV, Tariq A |
| 856 ## - ELECTRONIC LOCATION AND ACCESS | |
| DOI | <a href="https://dx.doi.org/10.1155/2014/728198">https://dx.doi.org/10.1155/2014/728198</a> |
| Public note | https://dx.doi.org/10.1155/2014/728198 |
| 942 ## - ADDED ENTRY ELEMENTS (KOHA) | |
| Koha item type | Journal Article |
| Item type description | Article |
| Withdrawn status | Lost status | Damaged status | Not for loan | Collection | Home library | Current library | Date acquired | Total Checkouts | Full call number | Barcode | Date last seen | Price effective from | Koha item type |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| MedStar Authors Catalog | MedStar Authors Catalog | 12/29/2020 | 25140269 | 25140269 | 12/29/2020 | 12/29/2020 | Journal Article |