Neuroimaging of nevoid basal cell carcinoma syndrome (NBCCS) in children. 

<br/><br/> Nevoid basal cell carcinoma syndrome (NBCCS, Gorlin syndrome) is an autosomal dominant condition with a wide range of manifestations, including multiple basal cell carcinomas, medulloblastoma, odontogenic keratocysts (OKC) and skeletal abnormalities. Children with NBCCS also have a predisposition for secondary cancers after exposure to ionising radiation. In children undergoing imaging for posterior fossa mass and/or maxillofacial cysts, certain additional findings can raise the possibility of NBCCS. Making the diagnosis can significantly impact patient management, especially for children with medulloblastoma. 
<br/><br/><br/>English 
<br/><br/><label>ISSN: </label>0301-0449 
<br/><br/><label>Subjects--Topical Terms: </label><br/>*Algorithms<br/>*Basal Cell Nevus Syndrome/di [Diagnosis]<br/>*Decision Support Systems, Clinical<br/>*Magnetic Resonance Imaging/mt [Methods]<br/>*Neuroimaging/mt [Methods]<br/>*Tomography, X-Ray Computed/mt [Methods]<br/>Adolescent<br/>Child<br/>Child, Preschool<br/>Diagnosis, Differential<br/>Female<br/>Humans<br/>Infant<br/>Infant, Newborn<br/>Male<br/>Reproducibility of Results<br/>Sensitivity and Specificity<br/>Young Adult
<br/><br/><label>Subjects--Geographic Terms: </label><br/>MedStar Washington Hospital Center
<br/><br/><label>Index Terms--Occupation: </label><br/>Medicine/Oral and Maxillofacial Surgery
<br/><br/><label>Index Terms--Function: </label><br/>Journal Article